Aortic atresia

  • associated with hypoplastic left heart syndrome
  • ascending aorta smaller than brachiocephalic artery
  • blood flows from heart to aorta via pulmonary trunk and persistent ductus. Arch fills retrograde
  • normal origin of brachiocephalics
  • coronaries arise from ascending aorta
  • survival depends on PDA patency
  • Norwood operation: converts morphological right ventricle into systemic ventricle, anastomosing pulmonary trunk to ascending aorta
  • blood flow to pulmonary arteries maintained through modified Blalock-Taussig shunt