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- Rare acute syndrome
- Subgroup of ADEM
- Subtype of anti-GQ1b IgG antibody syndrome
- Inflammation confined to brainstem
- Preceded by febrile illness
- Benign prognosis
- Ataxia, ocular paresis, impaired reflexes
- Pathogenesis uncertain
- No CSF oligoclonal bands
Imaging
- Extensive high T2 signal in midbrain and pons, sometimes in basal ganglia and thalamus
- Lesions resolve with time, good prognosis