Cardiac rhabdomyoma

  • 40% of benign neoplasms in infants and children
  • Usually seen less than 1 year age
  • Associated with tuberous sclerosis in 50% cases
  • Arrhythmias usually presenting feature
  • Inoperable – being deep seated, poorly demarcated and multiple
  • Most regress spontaneously 
Imaging
  • Intramural, more common in ventricles
  • Small and multiple
  • Avg 3 to 4 cm in diameter
  • ECHO: iso to hyper echoic 
  • CT: enhancing lesions, when multiple, appear as diffuse thickening of myocardium
  • MR: similar to myocardium on T1 and hyper intense on T2
Read more

Grebenc, Mary L., et al. “Primary cardiac and pericardial neoplasms: radiologic-pathologic correlation.” Radiographics 20.4 (2000): 1073-1103.

Umeoka, Shigeaki, et al. “Pictorial review of tuberous sclerosis in various organs.” Radiographics 28.7 (2008): e32.

Tao, Ting Y., et al. “Pediatric cardiac tumors: clinical and imaging features.” Radiographics 34.4 (2014): 1031-1046.