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- sclerosing mediastinitis or mediastinal fibrosis
- fibrous tissue and collagen in mediastinum
- sequel to infection from histoplasmosis or tuberculosis
- sarcoidosis, autoimmune diseases, retroperitoneal fibrosis, radiation, drugs (methysergide maleate)
- SVC obstruction, obstruction to central pulmonary artery or veins
- two types: focal or diffuse. Focal in tuberculous/ histoplasmosis. Diffuse in idiopathic form, associated with retroperitoneal fibrosis
- focal: calcified. diffuse: non calcified infiltrative
imaging
Chest xray
- non specific
- underestimates extent of disease
- TB or fungal infection may show calcified lymph nodes
CT
- infiltrative, extensively calcified hilar or mediastinal process
- focal in tuberculous or histoplasmosis
- diffuse in idiopathic form
MRI
- intermediate on T1
- variable signal on T2
- low signal in T2 seen in fibrous components, distinguishes from other conditions like malignancy
- heterogeneous enhancement post Gado
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