Mayer Rokitansky Küster Hauser syndrome

  • 1 in 4000-5000
  • second most common cause of primary infertility
  • vaginal agenesis or proximal and middle segment hyperplasia
  • intact ovaries and fallopian tubes
  • varying uterine anomalies – agenesis, hypoplasia, uni or bicornuate
  • renal agenesis, pelvic kidney
  • normal external genitalia
  • amenorrhea
  • cyclic pelvic pain