Type I
- parathyroid adenoma or hyperplasia (hyperparathyroidism)
- pancreatic islet cell tumors
- pituitary adenoma
Type II A
- parathyroid hyperplasia
- adrenal medullary tumor
- medullary thyroid cancer
Type II B
- medullary thyroid cancer
- adrenal medullary tumor
- marfanoid features, multiple cutaneous and mucosal neuromas, neurofibromas and gastrointestinal ganglioneuromas