- Young patients, peak in first decade
- Bilateral lesions diagnostic of neurofibromatosis type 1
- Pilocystic astrocytoma (WHO grade 1) most common. Little or no progression over time
- Visual loss less common in NF-1
Imaging
- Fusiform enlargement of optic nerve
- Expansion of optic canal
- MRI most accurate, iso to hypo on T1, hyper on T2 with variable enhancement
Read more
Chung, Ellen M., Charles S. Specht, and Jason W. Schroeder. “Pediatric orbit tumors and tumorlike lesions: neuroepithelial lesions of the ocular globe and optic nerve.” Radiographics 27.4 (2007): 1159-1186.
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