Rib notching

due to external pressure on rib

superior rib notching
  • connective tissue disease: rheumatoid arthritis, SLE, Sjogren, scleroderma
  • metabolic: hyperparathyroidism
  • neurofibromatosis
  • restrictive lung disease
  • poliomyelitis
  • Marfan syndrome
  • osteogenesis imperfecta
  • progeria
inferior rib notching
  • arterial: coarctation of aorta, aortic thrombosis, subclavian obstruction, cause of pulmonary oligemia
  • venous: superior vena cava obstruction
  • arteriovenous: pulmonary AV malformation, chest wall arterial malformation
  • neurogenic: neurofibromatosis (ribbon ribs)