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- juxta articular calcified soft tissue masses
- normal serum calcium and phosphorus
- no renal, metabolic or collagen vascular disease
- autosomal dominant
- abnormal phosphate reabsorption
- 1st-2nd decade
- M=F
- blacks
clinical
- progressive soft tissue mass with skin ulceration, sinus tract draining chalky milk like fluid
- swelling
- restricted motion
- hyperphosphatemia
- hypervitaminosis D
- normal serum calcium, ALP, renal function, parathyroid
- recurs after excision
imaging
- hip > elbow > shoulder > feet > ribs
- never seen in knees
- extensor surface of joints
- dense, loculated, multiglobular calcified soft tissue mass
- up to 20 cm size
- cystic appearance with radiolucent septa
- sedimentation sign – fluid fluid levels with milk of calcium
- normal bones