Aneurysmal dilatation of median prosencephalic vein of Markowski due to arteriovenous fistula that occurs in 6-11 weeks of gestation
30% of all pediatric vascular malformations
M:F = 2:1
Most common extra cardiac cause of high output cardiac failure
Presents with heart failure or hydrocephalus
Two types: choroidal and mural. Choroidal has feeders from pericallosal, choroidal or thalamoperforating arteries. Mural has few feeders from uni or bilateral collicular or posterior choroidal arteries
Imaging
Chest radiograph
Cardiomegaly
Wide mediastinum
CT
Plain study: venous pouch slightly hype dense. Wall calcification seen when there is thrombus in the aneurysm. Hydrocephalus, ischemia, parenchymal atrophy
